Multilobular biliary cirrhosis of the liver associated with cystic fibrosis (mucoviscidosis).

A case (including autopsy findings) is reported of multilobular biliary cirrhosis with 
a strictly nodular liver developing in a 20- year-old male with 
cystic fibrosis (mucoviscidosis). The pathogenesis of biliary cirrhosis in cystic fibrosis 
is briefly discussed. 