Lung function in children and young adults with cystic fibrosis.

The main characteristic of patients with cystic fibrosis is lung involvement; the 
fatal outcome of the disease is most often due to pulmonary 
complications. Since the paper by West et al. (1954) on pulmonary 
function in cystic fibrosis, the importance of lung function studies in 
this disorder has been stressed in several publications. We have studied 
lung function in a number of children and young adults with 
cystic fibrosis. The results have been correlated with clinical, radiological, and 
bacteriological findings. 