Gastrointestinal and nutritional manifestations of cystic fibrosis. pp. 83-111.

The purpose of this paper is to summarize the present state of 
our knowledge of the gastrointestinal manifestations and absorption and metabolism of 
nutrients in patients with cystic fibrosis. The gastrointestinal manifestations include pancreatic 
exocrine insufficiency, pancreatic calcification and stones, diabetes, liver and gall bladder 
abnormalities, intestinal obstruction, and complications of malabsorption. Nutritional aspects of cystic 
fibrosis include growth retardation and body composition, fat and nitrogen absorption, 
amino acid absorption, medium-chain triglyceride absorption, and deficiency of fat-soluble vitamins. 
The critical questions for projection into the future fall into three 
categories: intestinal absorption, gastrointestinal function and experimental design. 